Recent Papers on Rhabdomyosarcoma - 24 October 2014
From Google Scholar Alerts
Please note that some are abstracts requiring subscriptions or purchase of the full article, others provide a more comprehensive view of the paper.

Shorter-Duration Therapy Using Vincristine, Dactinomycin, and Lower-Dose Cyclophosphamide With or Without Radiotherapy for Patients With Newly Diagnosed Low-Risk Rhabdomyosarcoma: A Report From the Soft Tissue Sarcoma Committee of the Children's Oncology Group
DO Walterhouse, AS Pappo, JL Meza, JC Breneman… - Journal of Clinical Oncology, 2014
Purpose Intergroup Rhabdomyosarcoma Study Group (IRSG) studies III and IV showed
improved failure-free survival (FFS) rates with vincristine, dactinomycin, and
cyclophosphamide (VAC; total cumulative cyclophosphamide dose, 26.4 g/m 2) compared ...

Tumour volume reduction after neoadjuvant chemotherapy impacts outcome in localised embryonal rhabdomyosarcoma
TM Dantonello, M Stark, B Timmermann, J Fuchs… - Pediatric Blood & Cancer, 2014
Background Response (tumour volume reduction) to induction chemotherapy has been
used to stratify secondary local and systemic treatment of Intergroup Rhabdomyosarcoma
Study Group III (IRSG-III) embryonal rhabdomyosarcoma (RME) in consecutive CWS-trials ...

An extremely rare case of testicular malign
neoplasm; alveolar subtype of rhabdomyosarcoma
with long term follow-up

T Ipekci, Y Akin, B Hoscan, A Tunckiran - Journal of Health Sciences, 2014
Abstract Testicular neoplasm usually occur in men aged between 15 and 35. These are
solid organ tumours and also should be operated when there is a suspicious clinical
findings. Testis tumours are levelled after histopathology evaluation. The medical, surgical ...

P Banerjee, S Mukhopadhyay, N Pal, A Mukhopadhyay - Annals of Oncology, 2014
... Among total patients 42% were ALL, 12% were NHL, 6% were Hodgkin disease, 12% were
Rhabdomyosarcoma, 8% were PNET, 8% were Germ cell Tumor, 4% were brain tumor, 4%
were Osteosarcoma and rest 4% were soft tissue and other patients. ...

Brain Metastasis of Crystal-Deficient, CD68-Positive Alveolar Soft Part Sarcoma: Ultrastructural Features and Differential Diagnosis
MD Cykowski, J Hicks, DI Sandberg, A Olar, JA Bridge… - Ultrastructural Pathology, 2014
... metastasis. In the pediatric population, sarcomas metastatic to the CNS include
osteosarcoma, Ewing sarcoma/peripheral primitive neuroectodermal tumor,
rhabdomyosarcoma, clear cell sarcoma of soft tissue, and ASPS [15]. ...

The mammalian Hippo pathway: regulation and function of YAP1 and TAZ
M Kodaka, Y Hata - Cellular and Molecular Life Sciences, 2014

... The Hippo pathway and RASSF6 are simultaneously activated and accomplish tumor suppressive roles in a parallel manner. In alveolar rhabdomyosarcoma (aRMS), PAX3-FOXO enhances RASSF4 expression, which leads to MST1 inhibition and YAP1 activation [105]. ...

Analysis of Clinical Prognostic Factors for Adult Patients with Head and Neck Sarcomas
AE Chang, X Chai, SM Pollack, E Loggers, E Rodler… - Otolaryngology--Head and …, 2014
... org). Rhabdomyosarcoma (57%) had the lowest 2-year DSS rate. ... tumors. In our
series of adult patients, the most common histological subtypes were angiosarcoma,
osteosarcoma, chondrosarcoma, and rhabdomyosarcoma. ...

Pleomorphic Rhabdomyosarcoma Presenting as a Hypopharyngeal Mass
RA Crane, CM Johnson, GP Grice, DP Mullin, KK Bach - Head & Neck, 2014
Background: Rhabdomyosarcoma is a rare malignancy derived from skeletal muscle with
approximately 40% of cases involving the head and neck. The pleomorphic variant,
however, most commonly occurs in the extremities and has never, to our knowledge, been ...

A mistaken identity: rhabdomyosarcoma of the middle ear cleft misdiagnosed as chronic suppurative otitis media with temporal lobe abscess
M Muranjan, S Karande, S Parikh, S Sankhe - BMJ Case Reports, 2014
Summary A 5-year-old girl presented with a 3-month history of left side facial palsy, followed sequentially by purulent ear discharge, complete external ophthalmoplaegia and blurred vision. On clinical examination she was febrile with left-sided conductive hearing loss. She ...

Renal Liposarcoma in a Patient Undergoing Radiotherapy in Childhood: A Case Report
PN Aguiar Jr, B de Souza Gutierres, DP Guimaraes - Journal of Medical Cases, 2014
... the relevant literature. A 26-year-old male patient with a history of prostate
rhabdomyosarcoma that has been submitted to surgical resection and adjuvant
radiotherapy 23 years ago in the childhood was presented. He was asymptomatic ...

P Dokouhaki, P Graham, R Kanthan - Pathology-Journal of the RCPA, 2014
Page 1. Copyright İ Royal College of pathologists of Australasia. Unauthorized reproduction of this article is prohibited. Rhabdomyosarcoma (RMS) is the most common soft tissue sar- coma among children. The identification ...

Abstract: A case of an extremely unusual tumor of the larynx, pleomorphic
rhabdomyosarcoma, is presented with a review of literature. This is the fifth case of this
malignancy described in the larynx in the English language literature. A histopathological ...

Parental Military Service, Agent Orange Exposure, and the Risk of Rhabdomyosarcoma in Offspring
S Grufferman, PJ Lupo, RI Vogel, HE Danysh… - Journal of Pediatrics
Objective To evaluate the role of parental military service-related exposures and
rhabdomyosarcoma (RMS) risk in offspring using data from a large case-control study of
childhood RMS. Study design Cases (n= 319) were enrolled from the third trial run by the ...

Structural Analysis of the Human Fibroblast Growth Factor Receptor 4 Kinase.
E Lesca, A Lammens, R Huber, M Augustin - Journal of molecular biology, 2014
... variety of pathological disorders. FGFR4 is involved in myogenesis and muscle
regeneration. Mutations affecting the kinase domain of FGFR4 may cause cancer
eg breast cancer or rhabdomyosarcoma. Whereas FGFRs 1-3 ...

Case in Point: Alveolar Rhabdomyosarcoma: A Rare Malignancy Presenting as Hypertension
N Verzosa, S Deese, H Kendhari
A biopsy sample of the mass was obtained, and pathology test results (Figure 3) were positive for myogenin, a specific marker for rhabdomyosarcoma (RMS). ...